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色素性静脉旁脉络膜视网膜萎缩中的视网膜微血管病变。

Retinal microangiopathy in pigmented paravenous chorioretinal atrophy.

作者信息

Limaye S R, Mahmood M A

机构信息

Ophthalmology Service, DC General Hospital, Washington 20003.

出版信息

Br J Ophthalmol. 1987 Oct;71(10):757-61. doi: 10.1136/bjo.71.10.757.

DOI:10.1136/bjo.71.10.757
PMID:3676145
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1041301/
Abstract

This report describes an atypical case of pigmented paravenous chorioretinal atrophy, associated with focal progressive peripheral retinal microangiopathy, in a 51-year-old black female. The eyes were asymmetrically involved. Although several cases have been reported with typical features of this uncommon entity, none of them have been known to be associated with retinal microangiopathy. The occurrence of such microangiopathy supports the hypothesis that damage to the retinal photoreceptors may induce retinal microangiopathy, as suggested in other clinical and experimental studies.

摘要

本报告描述了一名51岁黑人女性患色素性静脉旁脉络膜视网膜萎缩的非典型病例,该病例伴有局灶性进行性周边视网膜微血管病变。双眼受累不对称。尽管已有数例报告具有这种罕见病症的典型特征,但均未发现与视网膜微血管病变相关。这种微血管病变的出现支持了如下假说:正如其他临床和实验研究中所提示的,视网膜光感受器受损可能诱发视网膜微血管病变。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/56205180a001/brjopthal00620-0036-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/e769bdcde4b0/brjopthal00620-0037-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/1355a1bcbb57/brjopthal00620-0037-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/2853be9c8d9b/brjopthal00620-0037-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/81a4671ffd0f/brjopthal00620-0035-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/4d63f666edb9/brjopthal00620-0036-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/56205180a001/brjopthal00620-0036-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/e769bdcde4b0/brjopthal00620-0037-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/1355a1bcbb57/brjopthal00620-0037-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/2853be9c8d9b/brjopthal00620-0037-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/81a4671ffd0f/brjopthal00620-0035-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/4d63f666edb9/brjopthal00620-0036-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4dec/1041301/56205180a001/brjopthal00620-0036-b.jpg

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本文引用的文献

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RETINO-CHOROIDITIS RADIATA.放射性视网膜脉络膜炎
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2
A curious affection of the fundus oculi: helicoid peripapillar chorioretinal degeneration. Its relation to pigmentary paravenous chorioretinal degeneration.一种奇特的眼底病变:螺旋状视乳头周围脉络膜视网膜变性。它与色素性静脉旁脉络膜视网膜变性的关系。
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Telangiectasia and optic atrophy in cone-rod degenerations.视锥-视杆细胞营养不良中的毛细血管扩张和视神经萎缩
色素性静脉旁视网膜脉络膜萎缩(综述)
Exp Ther Med. 2014 Jun;7(6):1439-1445. doi: 10.3892/etm.2014.1648. Epub 2014 Mar 28.
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Pigmented paravenous chorioretinal atrophy with Coat's like response.色素性脉络膜视网膜旁萎缩伴 Coat 样反应。
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Pigmented paravenous chorioretinal atrophy.色素性静脉旁脉络膜视网膜萎缩
Am J Ophthalmol. 1983 Sep;96(3):338-44. doi: 10.1016/s0002-9394(14)77825-0.
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Retinal vascular changes in hereditary visual cell degeneration.遗传性视觉细胞变性中的视网膜血管变化。
Arch Ophthalmol. 1969 Jan;81(1):99-105. doi: 10.1001/archopht.1969.00990010101014.
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Retinal vascular changes following toxic effects on visual cells and pigment epithelium.视觉细胞和色素上皮受到毒性作用后视网膜血管的变化。
Arch Ophthalmol. 1969 Jan;81(1):106-14. doi: 10.1001/archopht.1969.00990010108015.
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Pigmented paravenous retinochorodial atrophy.色素性静脉旁视网膜脉络膜萎缩
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