Wu Keng-Liang, Changchien Chi-Sin, Kuo Chung-Mou, Chuah Seng-Kee, Chiu Yi-Chun, Kuo Chung-Huang
Division of Gastroenterology, Department of Internal Medicine, Chang Gung Memorial Hospital, Kaohsiung, Taiwan.
Eur J Gastroenterol Hepatol. 2002 Dec;14(12):1397-9. doi: 10.1097/00042737-200212000-00019.
A 26-year-old man had suffered from several episodes of right upper-quadrant pain for 6 months. Abdominal ultrasonography showed multiple saccular dilatations of the intrahepatic biliary tract, with hepatolithiasis at the bilateral hepatic lobe. Abdominal computed tomography also revealed saccularly dilated intrahepatic ducts with hepatolithiasis. Communication between saccular dilatations of the intrahepatic biliary tract and normal bile ducts was demonstrated by endoscopic retrograde cholangiopancreatography. Choledochal cyst type V (Caroli's disease) was diagnosed. The patient's 29-year-old sister was also diagnosed with Caroli's disease based on abdominal sonography. An ultrasonography survey was carried out on the family. Reports of Caroli's disease occurring in two siblings are rare in the literature.
一名26岁男性右上腹疼痛发作数次，持续6个月。腹部超声显示肝内胆管多发囊状扩张，双侧肝叶有肝内胆管结石。腹部计算机断层扫描也显示肝内胆管囊状扩张伴肝内胆管结石。内镜逆行胰胆管造影显示肝内胆管囊状扩张与正常胆管之间有交通。诊断为V型胆管囊肿（卡罗利病）。患者29岁的姐姐经腹部超声检查也被诊断为卡罗利病。对该家族进行了超声检查。文献中罕见两兄弟均患卡罗利病的报道。
