Willermain François, Greiner Kathrin, Forrester John V
Department of Ophthalmology, University of Aberdeen, Scotland, UK
Ocul Immunol Inflamm. 2003 Dec;11(4):305-7. doi: 10.1076/ocii.11.4.305.18271.
To describe a patient with birdshot retinochoroidopathy with peripheral pigmentary changes mimicking a pseudo-retinitis pigmentosa fundus.
A 60-year-old female patient was referred for bilateral uveitis. Fundus examination showed several creamy lesions in the choroid of both eyes. The patient was HLA-A29-positive. A diagnosis of birdshot choroidopathy was made and she was treated with immunosupressive agents. Six years later, a pigmentation of the retina was noted in both eyes, which progressed to a bone-shaped appearance.
Pigmentary reaction is a common feature of retinal lesions, although it rarely takes on a retinitis pigmentosa-like appearance. Furthermore, birdshot fundus lesions do not usually become highly hyperpigmented even after long-term evolution. This pigmentation may represent one type of the end-stage of birdshot retinochoroidopathy.