Spiegel R, Miron D, Fink D, Gavriel H, Horovitz Y
Pediatric Department A, HaEmek Medical Center, Afula, Rappaport School of Medicine, Technion, Haifa, Israel.
Pediatr Cardiol. 2004 Nov-Dec;25(6):690-2. doi: 10.1007/s00246-003-0664-3.
We describe an 18-month-old child with idiopathic hypereosinophilic syndrome (IHES) who presented with fever, and cervical lymphadenopathy. Chest X-ray showed marked cardiomegaly, and echocardiogram revealed large pericardial effusion. Other causes of pericarditis were excluded. Despite the initiation of steroid therapy, signs of impending cardiac tamponade developed. Pericardiocentesis yielded bloody fluid with a white blood count of 14,800/mm3, of which 23% were eosinophils. The child recovered after pericardial drainage and prolonged systemic steroid therapy. Eosinophilic pericarditis is a rare but potentially dangerous complication of IHES.
我们描述了一名18个月大患有特发性高嗜酸性粒细胞综合征(IHES)的儿童,其表现为发热和颈部淋巴结肿大。胸部X线显示明显的心脏扩大,超声心动图显示大量心包积液。排除了心包炎的其他病因。尽管开始了类固醇治疗,但仍出现了心脏压塞的迹象。心包穿刺抽出了血性液体,白细胞计数为14,800/mm³,其中23%为嗜酸性粒细胞。该患儿在心包引流和长期全身性类固醇治疗后康复。嗜酸性粒细胞性心包炎是IHES一种罕见但潜在危险的并发症。