Fioravanti A, Godano U, Consales A, Mascari C, Calbucci F
Department of Neurosurgery, Bellaria Hospital, Via Altura n. 3, 40139 Bologna, Italy.
Childs Nerv Syst. 2004 Oct;20(10):770-3. doi: 10.1007/s00381-004-0925-3.
We report two cases of bobble-head doll syndrome associated with a large suprasellar arachnoid cyst successfully treated with a minimally invasive endoscopic approach.
The clinical history, surgical treatment and results of two children, a 9-year-old boy and a 1-year-old girl, both presenting the clinical features of the bobble-head doll syndrome, are described. As a first procedure, a ventriculo-cystostomy was endoscopically performed in both patients, obtaining either resolution of the symptoms or notable cyst reduction. In the girl, a re-closure of the stoma, with cyst re-expansion, was observed after 18 months. She then underwent a second procedure, a ventriculo-cysto-cisternostomy, with a good result. After 3 years' follow-up, the neurological condition of both patients remains good with complete resolution of abnormal head movement.
In our opinion, endoscopic treatment is the procedure of choice for this condition, as it involves few complications and gives good results.
我们报告两例与鞍上大蛛网膜囊肿相关的点头娃娃综合征患者，采用微创内镜方法成功治疗。
描述了一名9岁男孩和一名1岁女孩这两名儿童的临床病史、手术治疗及结果，他们均表现出点头娃娃综合征的临床特征。作为首要手术，两名患者均在内镜下进行了脑室 - 囊肿造瘘术，症状得以缓解或囊肿显著缩小。在女孩中，18个月后观察到造瘘口重新闭合，囊肿再次扩大。随后她接受了第二次手术，即脑室 - 囊肿 - 脑池造瘘术，效果良好。经过3年随访，两名患者的神经状况良好，异常头部运动完全消失。
我们认为，内镜治疗是这种疾病的首选治疗方法，因为它并发症少且效果良好。
