Chin Shy-Chyi, Fatterpeckar Girish, Kao Chuan-Hsiang, Chen Cheng-Yu, Som Peter M
Department of Radiology, Tri-Service General, Hospital, Taipei, Taiwan.
AJNR Am J Neuroradiol. 2004 Apr;25(4):636-8.
Localized amyloidosis is an uncommon benign disorder. The purpose of this report is to present the case of a 21-year-old man who had localized amyloidosis simultaneously involving the sinonasal cavities and the larynx. The rarer sinonasal lesion demonstrated CT findings of adjacent "fluffy" bone changes, possibly representing a new finding suggestive of this disorder. At MR imaging, the amyloid had signal intensity similar to that of skeletal muscle on T1- and T2-weighted images. After contrast material administration, the amyloid enhanced at most minimally, but peripheral enhancement about the mass was present. The importance of this case lies in the multifocal presentation of this uncommon disorder, and the imaging findings herein may provide a new sign of this paranasal sinus disease.
局限性淀粉样变性是一种罕见的良性疾病。本报告旨在介绍一名21岁男性病例,该患者同时患有累及鼻窦腔和喉部的局限性淀粉样变性。较为罕见的鼻窦病变在CT上表现为相邻骨质呈“絮状”改变,这可能是提示该疾病的一项新发现。在磁共振成像(MR)上,淀粉样物质在T1加权像和T2加权像上的信号强度与骨骼肌相似。注射对比剂后,淀粉样物质最多仅有轻微强化,但肿块周围有强化。该病例的重要性在于这种罕见疾病的多灶性表现,且本文的影像学表现可能为这种鼻窦疾病提供一个新的征象。