门肺高压

Portopulmonary hypertension.

作者信息

Passarella Michael, Fallon Michael B, Kawut Steven M

机构信息

Department of Medicine, University of Alabama at Birmingham, BDB 327, 1530 3rd Avenue S., Birmingham, AL 35294, USA.

出版信息

Clin Liver Dis. 2006 Aug;10(3):653-63, x. doi: 10.1016/j.cld.2006.08.023.

DOI:10.1016/j.cld.2006.08.023

PMID:17162233

Abstract

Portopulmonary hypertension is a common condition in patients who have portal hypertension. This article reviews the definition and clinical presentation of this disorder and outlines our current understanding of its pathophysiology. A diagnostic approach is provided , and novel medical therapies that are being investigated to treat this condition are discussed. Finally, the safety of liver transplantation in patients who have portopulmonary hypertension is reviewed.

摘要

门肺高压是门静脉高压患者中的一种常见病症。本文回顾了这种病症的定义和临床表现，并概述了我们目前对其病理生理学的理解。提供了一种诊断方法，并讨论了正在研究用于治疗这种病症的新型药物疗法。最后，回顾了门肺高压患者肝移植的安全性。