Celikel Cigdem, Yumuk P Fulden, Basaran Gul, Yildizeli Bedrettin, Kodalli Nihat, Ahiskali Rengin
Department of Pathology, Marmara University School of Medicine, Istanbul, Turkey.
APMIS. 2007 Jul;115(7):881-8. doi: 10.1111/j.1600-0463.2007.apm_727.x.
Epithelioid hemangioendothelioma is a rare vascular neoplasm of uncertain malignant potential. Various reports document metastatic or concurrent epithelioid hemangioendothelioma in several sites, most commonly with combined lung and liver involvement. The concurrent involvement of multiple sites at presentation may cause diagnostic problems because epithelioid hemangioendothelioma can mimic other neoplastic processes. Although it is a chemo-resistant disease, chemotherapy is usually advised for patients with metastatic or concurrent involvement. Here we document the presentation, treatment, and outcome of two cases with concurrent involvement of the lung and liver.
上皮样血管内皮瘤是一种恶性潜能不确定的罕见血管肿瘤。各种报告记录了在多个部位出现转移性或同时性上皮样血管内皮瘤的情况，最常见的是肺和肝同时受累。就诊时多个部位同时受累可能会导致诊断问题，因为上皮样血管内皮瘤可能会模仿其他肿瘤过程。尽管它是一种化疗耐药性疾病，但通常建议对有转移或同时受累的患者进行化疗。在此，我们记录了两例肺和肝同时受累患者的临床表现、治疗及预后情况。
