Rosengarten Dror, Kramer Mordechai R, Amir Gail, Fuks Leonardo, Berkman Neville
Institute of Pulmonology, Hadassah-Hebrew University Medical Center, Jerusalem, Israel.
Isr Med Assoc J. 2011 Nov;13(11):676-9.
Pulmonary epithelioid hemangioendothelioma (PEH), previously known as "intravascular bronchoalveolar tumor," is a rare vascular malignancy with an unpredictable prognosis. Treatment can vary from observation in asymptomatic patients to surgery in patients with resectable disease or chemotherapy in patients with disseminated disease. This report describes the clinical, radiological and pathological features of three cases of PEH and a review of the current literature.
肺上皮样血管内皮瘤(PEH),以前称为“血管内支气管肺泡瘤”,是一种罕见的血管恶性肿瘤,预后不可预测。治疗方法因患者情况而异,无症状患者可观察,可切除疾病患者可行手术,播散性疾病患者可行化疗。本报告描述了3例PEH的临床、放射学和病理学特征,并对当前文献进行了综述。