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POEMS syndrome in a 15-year-old boy: radiological findings.

作者信息

Lanza Cecilia, Misericordia Marco, Fabrizzi Giancarlo

机构信息

Paediatric Radiology Department, Azienda Ospedaliero-Universitaria Ospedali Riuniti, via Corridoni 11, Ancona, 60123, Italy.

出版信息

Pediatr Radiol. 2007 Nov;37(11):1147-50. doi: 10.1007/s00247-007-0561-7. Epub 2007 Sep 18.

DOI:10.1007/s00247-007-0561-7
PMID:17876573
Abstract

POEMS syndrome is a multisystem disorder related to a plasma-cell dyscrasia. It is usually seen between the ages of 40 and 50 years and is very rare in childhood. Radiologically, this syndrome is characterized by sclerotic focal bone lesions with a normal radionuclide bone scan. We report a case of POEMS syndrome in a 15-year-old boy in whom plain radiographs and multidetector-row spiral CT (MDCT) provided information that was helpful in the clinical assessment.

摘要

相似文献

1
POEMS syndrome in a 15-year-old boy: radiological findings.
Pediatr Radiol. 2007 Nov;37(11):1147-50. doi: 10.1007/s00247-007-0561-7. Epub 2007 Sep 18.
2
POEMS syndrome: unusual radiographic, scintigraphic and CT features.POEMS综合征:不寻常的放射学、闪烁扫描和CT特征。
Eur Radiol. 1998;8(1):134-6. doi: 10.1007/s003300050353.
3
Computed tomography assessment of bone lesions in patients with POEMS syndrome.POEMS综合征患者骨病变的计算机断层扫描评估
Eur Radiol. 2015 Feb;25(2):497-504. doi: 10.1007/s00330-014-3428-y. Epub 2014 Sep 25.
4
CT characteristics in 24 patients with POEMS syndrome.24例POEMS综合征患者的CT特征
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5
[Usefulness of (18)F-FDG PET/CT for detecting lesions in patients with POEMS syndrome].[(18)F-FDG PET/CT在POEMS综合征患者病变检测中的应用价值]
Rinsho Ketsueki. 2012 Dec;53(12):2013-7.
6
Plasma-cell dyscrasia with polyneuropathy. The spectrum of POEMS syndrome.伴有多发性神经病的浆细胞异常增生症。POEMS综合征的范围。
N Engl J Med. 1992 Dec 31;327(27):1919-23. doi: 10.1056/NEJM199212313272705.
7
[POEMS syndrome].[POEMS综合征]
Radiologe. 1995 Aug;35(8):528-30.
8
Detection of bone lesions by CT in POEMS syndrome.
Intern Med. 2011;50(13):1393-6. doi: 10.2169/internalmedicine.50.5263. Epub 2011 Jul 1.
9
Ultrasound evaluation of peripheral neuropathy in POEMS syndrome.POEMS 综合征周围神经病的超声评估。
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10
Usefulness of F-18 FDG PET/CT in the follow-up of POEMS syndrome after autologous peripheral blood stem cell transplantation.自体造血干细胞移植后 POEMS 综合征的 F-18 FDG PET/CT 随访的应用价值。
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POEMS syndrome: definitions and long-term outcome.POEMS综合征:定义与长期预后
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