Arribas-Garcia Ignacio, Domínguez Manuel Fernández, Alcalá-Galiano Andrea, García Antonio Fernández, Valls Julio Castedo, De Rasche Enrique Niembro
Department of Maxillofacial Surgery, Hospital Monteprincipe, Madrid, Spain.
Head Neck. 2008 Oct;30(10):1384-8. doi: 10.1002/hed.20773.
Angiosarcomas are rare soft tissue malignant tumors with dismal prognosis. Head and neck involvement is uncommon (5%) and usually affects the scalp or facial skin.
We present the case of an inferior lip mucosal low-grade angiosarcoma in a 15-year-old boy treated exclusively with surgery. One and a half years after treatment, the patient was free of signs of recurrence. Prompt and accurate diagnosis with adequate imaging modalities and multidisciplinary treatment are crucial for optimal management of these neoplasms.
Lip mucosal involvement is exceptional with only a few cases described in the literature, all in patients older than 60 years To our knowledge, this is the youngest patient ever reported.
血管肉瘤是罕见的软组织恶性肿瘤,预后较差。头颈部受累并不常见(5%),通常累及头皮或面部皮肤。
我们报告了一例15岁男孩下唇黏膜低度血管肉瘤的病例,仅接受了手术治疗。治疗后一年半,患者无复发迹象。采用适当的影像学检查手段进行及时准确的诊断以及多学科治疗对于这些肿瘤的最佳管理至关重要。
唇部黏膜受累情况罕见,文献中仅描述了少数病例,所有病例患者均年龄大于60岁。据我们所知,这是有报道以来最年轻的患者。