Costa Dailana Louvain Marinho, Moura Heloisa Helena, Rodrigues Rosangela, Pineiro-Maceira Juan, Ramos-E-Silva Marcia
Federal University of Rio de Janeiro, Rio de Janeiro, Brazil.
J Clin Aesthet Dermatol. 2011 Oct;4(10):52-4.
The authors present a case of telangiectasia macularis eruptiva perstans, an uncommon form of cutaneous mastocytosis, in a 53-year-old man and discuss its clinics, pathophysiology, laboratory results, and treatment. Cutaneous mastocytosis is a proliferation of masts cells on the skin without involvement of other organs. Typically the lesions of telangiectasia macularis eruptiva perstans are telangiectatic macules with color ranging from light to dark brown. It is more frequent in adults, with some reports in children. It is usually insidious, without symptoms at the beginning and, although a manifestation of cutaneous mastocytosis, telangiectasia macularis eruptiva perstans may present systemic involvement. It is very important for dermatologists to know this form of cutaneous mastocytosis and to make an early diagnosis, so they may treat the disorder and improve their patients' quality of life.
作者报告了一例持久性斑疹性毛细血管扩张症，这是一种罕见的皮肤肥大细胞增多症，患者为一名53岁男性，并讨论了其临床症状、病理生理学、实验室检查结果及治疗方法。皮肤肥大细胞增多症是指皮肤中肥大细胞增殖而不涉及其他器官。持久性斑疹性毛细血管扩张症的典型皮损为毛细血管扩张性斑疹，颜色从浅褐色到深褐色不等。该病在成人中更为常见，也有儿童病例的报道。它通常起病隐匿，起初没有症状，尽管是皮肤肥大细胞增多症的一种表现，但持久性斑疹性毛细血管扩张症可能会出现全身受累。皮肤科医生了解这种皮肤肥大细胞增多症并早期诊断非常重要，这样他们就可以治疗该疾病并提高患者的生活质量。
