Department of Radiology and Nuclear Medicine, Jordan University Hospital, Amman, Jordan.
Br J Radiol. 2010 Jan;83(985):e10-3. doi: 10.1259/bjr/14078580.
Odontogenic myxofibroma of the temporomandibular joint (TMJ) is a rare tumour; moreover, primary splenic angiosarcoma (PAS) in paediatric patients is extremely rare. We report on a 15-year-old boy who presented with right TMJ swelling and subsequently developed epigastric and right upper quadrant pain. The TMJ swelling proved to be odontogenic myxofibroma and the abdominal pain was a result of primary splenic angiosarcoma with hepatic metastasis. We report for the first time the synchronous presentation of PAS and odontogenic myxofibroma in a paediatric patient, and we describe the radiological features along with the histological diagnosis and clinical outcome. Uptake in (18)F-2-fluoro-2-deoxy-D-glucose positron emission tomography is also described for the first time for both these tumours.
颞下颌关节（TMJ）的牙源性黏液纤维瘤是一种罕见的肿瘤；此外，儿童原发性脾血管肉瘤（PAS）极为罕见。我们报告了一名 15 岁男孩，他最初表现为右侧 TMJ 肿胀，随后出现上腹部和右上腹疼痛。TMJ 肿胀被证实为牙源性黏液纤维瘤，而腹痛是原发性脾血管肉瘤伴肝转移的结果。我们首次报告了 PAS 和牙源性黏液纤维瘤在儿童患者中的同时出现，并描述了放射学特征以及组织学诊断和临床结果。我们还首次描述了这两种肿瘤的（18）F-2-氟-2-脱氧-D-葡萄糖正电子发射断层扫描摄取情况。
