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新生儿主动脉-心室通道:基于横断面和彩色多普勒超声检查的诊断与管理

Aortic-ventricular tunnel in a neonate: diagnosis and management based on cross sectional and colour Doppler ultrasonography.

作者信息

Sreeram N, Franks R, Walsh K

机构信息

Heart Clinic, Royal Liverpool Children's Hospital.

出版信息

Br Heart J. 1991 Mar;65(3):161-2. doi: 10.1136/hrt.65.3.161.

DOI:10.1136/hrt.65.3.161
PMID:2015126
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1024542/
Abstract

A five day old symptom free neonate was referred for assessment of a to and fro murmur associated with large volume pulses. Cross sectional echocardiography and colour flow mapping confirmed the diagnosis of an aortic-ventricular tunnel with forward flow into the aorta and regurgitant flow into the ventricle through both the tunnel and the dilated aortic valve ring. Surgical correction by patch closure of the aortic end of the tunnel was successfully undertaken two weeks later without any additional investigations. Postoperative echocardiography and colour flow imaging showed no aortic regurgitation and normal left ventricular dimensions and function.

摘要

一名出生五天、无症状的新生儿因与大量脉搏相关的来回杂音而被转诊进行评估。横断面超声心动图和彩色血流图证实诊断为主动脉 - 心室通道,血液向前流入主动脉,并通过通道和扩张的主动脉瓣环反流回心室。两周后成功进行了手术矫正,通过补片封闭通道的主动脉端,未进行任何额外检查。术后超声心动图和彩色血流成像显示无主动脉反流,左心室大小和功能正常。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d8fc/1024542/d63a402222b2/brheartj00039-0050-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d8fc/1024542/014a5e5325ba/brheartj00039-0049-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d8fc/1024542/d63a402222b2/brheartj00039-0050-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d8fc/1024542/014a5e5325ba/brheartj00039-0049-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d8fc/1024542/d63a402222b2/brheartj00039-0050-a.jpg

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Aorto-Left Ventricular Tunnel: The First Systematic Review of An Uncommon Entity (177 Worldwide Cases from 1965 to 2024).主动脉-左心室隧道:对一种罕见病症的首次系统综述(1965年至2024年全球177例病例)
Rev Cardiovasc Med. 2025 Feb 20;26(2):26005. doi: 10.31083/RCM26005. eCollection 2025 Feb.
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本文引用的文献

1
Aortico-left ventricular tunnel: collective review.
J Thorac Cardiovasc Surg. 1982 Jul;84(1):102-9.
2
Aorto-left ventricular communication after closure. Late postoperative problems.闭合术后的主动脉-左心室交通。术后晚期问题。
Br Heart J. 1983 May;49(5):501-6. doi: 10.1136/hrt.49.5.501.
3
Pulsed Doppler and two-dimensional echocardiographic findings in aortico-left ventricular tunnel.主动脉-左心室通道的脉冲多普勒及二维超声心动图表现
J Am Coll Cardiol. 1984 Nov;4(5):1012-4. doi: 10.1016/s0735-1097(84)80064-9.
4
Aorto-left ventricular tunnel. Clinical features and surgical management.主动脉左心室隧道。临床特征与手术治疗
Br Heart J. 1974 Apr;36(4):321-8. doi: 10.1136/hrt.36.4.321.
5
Correction of aortico-left ventricular tunnel during the first day of life.出生第一天行主动脉-左心室隧道矫治术。
Ann Thorac Surg. 1989 Feb;47(2):254-6. doi: 10.1016/0003-4975(89)90282-8.
6
Successful surgical treatment of an aortico--left ventricular tunnel in a four-month-old infant.
J Thorac Cardiovasc Surg. 1979 Jul;78(1):35-8.