Hucin B, Horvath P, Skovránek J, Reich O, Samánek M
Pediatric Cardiac Center, University Hospital Motol, Prague, Czechoslovakia.
Ann Thorac Surg. 1989 Feb;47(2):254-6. doi: 10.1016/0003-4975(89)90282-8.
Two critically ill newborns with aortico-left ventricular tunnel and severe heart failure were operated on at six and 14 hours after birth. The diagnosis was established clinically by the auscultatory finding of systolic and diastolic murmurs and by two-dimensional and Doppler echocardiography. In the first newborn, the left aortic sinus was connected with the left ventricle below the aortic valve by an aneurysmatically dilated tunnel. In the second patient, the tunnel connected the right aortic sinus and the left ventricle. The repair was performed under deep hypothermia, total hemodilution, and cardiopulmonary bypass. The tunnel was closed with two patches of Gore-Tex on the aortic and ventricular orifices. Both children are free from symptoms and are developing normally 10 and 8 months after repair.
两名患有主动脉-左心室通道及严重心力衰竭的危重新生儿分别在出生后6小时和14小时接受了手术。临床诊断依据听诊发现的收缩期和舒张期杂音以及二维和多普勒超声心动图来确定。在第一名新生儿中,左主动脉窦通过一个呈瘤样扩张的通道与主动脉瓣下方的左心室相连。在第二名患儿中,通道连接右主动脉窦和左心室。手术在深度低温、完全血液稀释及体外循环下进行。通过在主动脉和心室开口处使用两片戈尔特斯补片封闭通道。两名患儿均无症状,在修复术后10个月和8个月时发育正常。