Riberi A, Gariboldi V, Grisoli D, Collart F
Service de Chirurgie Cardiaque Adulte, Hôpital de la Timone, 264 rue Saint-Pierre, 13005 Marseille, France.
Rev Pneumol Clin. 2010 Feb;66(1):95-103. doi: 10.1016/j.pneumo.2009.12.012. Epub 2010 Feb 18.
Primary cardiac tumor is a rare disease, with an incidence ranging from 0.001 to 0.03%. Eighty percent of them are benign tumors, and among them 70% are myxomas, the others are: fibroelastoma, rhabdomyoma, fibroma, angioma and lipoma. Primary malignant tumors of heart are in 95% of cases sarcomas, the remaining 5% are lymphomas. Cardiac's metastases are more frequent than primary tumors. Diagnosis is made by echocardiography TAC and MRI. Whereas surgery is indicated in patients with benign tumors, or localised sarcomas, chemotherapy in those with widespread disease and radiotherapy and chemotherapy in lymphoma. Prognosis is excellent in benign cardiac tumor. Mean survival for sarcomas is 11 months, and lymphoma 5 years.
原发性心脏肿瘤是一种罕见疾病,发病率在0.001%至0.03%之间。其中80%为良性肿瘤,其中70%是黏液瘤,其他的有:纤维弹性瘤、横纹肌瘤、纤维瘤、血管瘤和脂肪瘤。心脏原发性恶性肿瘤95%为肉瘤,其余5%为淋巴瘤。心脏转移瘤比原发性肿瘤更常见。通过超声心动图、计算机断层扫描(TAC)和磁共振成像(MRI)进行诊断。良性肿瘤患者或局限性肉瘤患者适合手术治疗,广泛病变患者适合化疗,淋巴瘤患者适合放疗和化疗。良性心脏肿瘤的预后极佳。肉瘤的平均生存期为11个月,淋巴瘤为5年。