Azevedo Olga, Almeida Jorge, Nolasco Tânia, Medeiros Rosa, Casanova Jorge, Bartosch Carla, Almeida João, Pinho Paulo
Cardiology Department, Centro Hospitalar do Alto Ave - Unidade de Guimarães, Guimarães, Portugal.
Cardiovasc Ultrasound. 2010 Jun 18;8:23. doi: 10.1186/1476-7120-8-23.
Primary heart neoplasms are rare occurring with an estimated incidence of 0.0017-0.19%. Myxoma is the most prevalent primary heart tumor. The right atrium is an unusual localization, occurring only in 15-20% of myxoma cases. We report a rare case of a massive right atrial myxoma causing tricuspid valve obstruction and presenting as syncope and exertional dyspnea. This case illustrates the influence of myxoma's size, position and mobility as well as patient's body posture and respiration to the development of signs and symptoms. Three-dimensional echocardiography proved useful in surgery planning, allowing a better definition of the tumor outline and attachment.
原发性心脏肿瘤很罕见，估计发病率为0.0017 - 0.19%。黏液瘤是最常见的原发性心脏肿瘤。右心房是不常见的发病部位，仅在15 - 20%的黏液瘤病例中出现。我们报告一例罕见的巨大右心房黏液瘤病例，该肿瘤导致三尖瓣梗阻，表现为晕厥和劳力性呼吸困难。该病例说明了黏液瘤的大小、位置和活动度以及患者的体位和呼吸对症状和体征发展的影响。三维超声心动图在手术规划中证明很有用，能更好地明确肿瘤轮廓和附着情况。
