van Winden Marianne, Salu Paul
Departement Oogheelkunde, UZ Brussel, Vrije Universiteit Brussel, VUB, Laarbeeklaan 101, 1090, Jette, Belgium.
Doc Ophthalmol. 2010 Dec;121(3):223-9. doi: 10.1007/s10633-010-9244-z. Epub 2010 Aug 26.
A 19-year-old woman presented with subacute encephalopathy and subsequently developed hearing loss and occlusions of branches of the central retinal artery. The triad of microangiopathy of the brain, retina and cochlea is typical for Susac syndrome. The etiology of this syndrome is still unknown, but the prognosis is good in most cases. Spontaneous resolution usually occurs, but early treatment minimizes the risk of sequelae. Multifocal ERG may be useful to assess subclinical retinal dysfunction after recovery of subjective symptoms of BRAO in Susac syndrome.
一名19岁女性出现亚急性脑病,随后出现听力丧失和视网膜中央动脉分支阻塞。脑、视网膜和耳蜗微血管病变三联征是Susac综合征的典型表现。该综合征的病因尚不清楚,但大多数病例预后良好。通常会自发缓解,但早期治疗可将后遗症风险降至最低。多焦视网膜电图可能有助于评估Susac综合征中分支视网膜动脉阻塞主观症状恢复后亚临床视网膜功能障碍。