1st Department of Internal Medicine, Comenius University in Bratislava, Bratislava, Slovakia.
Rheumatol Int. 2012 Mar;32(3):675-8. doi: 10.1007/s00296-010-1676-y. Epub 2010 Dec 7.
A 62-year-old man presented with diabetes insipidus, pulmonary fibrosis, right atrial tumor and bilateral knee osteoarthritis with cystic lesions of distal femur and proximal tibia. Scintigraphy and histological examination of right femur bone biopsy revealed changes characterized for Paget's disease. Re-evaluation of the computer tomography (CT) scans and histological samples revealed diffuse infiltrates of foamy histiocytes in the bone marrow what was consistent with Erdheim-Chester disease. Positron emission tomography/computed tomography (PET/CT) was performed to access the activity and extent of disease.
一位 62 岁男性，表现为尿崩症、肺纤维化、右心房肿瘤和双侧膝关节骨关节炎，同时伴有股骨远端和胫骨近端囊性病变。右腿股骨骨活检的闪烁扫描和组织学检查显示符合 Paget 病的改变。对计算机断层扫描（CT）扫描和组织样本的重新评估显示骨髓中泡沫状组织细胞弥漫浸润，符合 Erdheim-Chester 病。进行正电子发射断层扫描/计算机断层扫描（PET/CT）以评估疾病的活性和范围。
