Medical School of Marília, FAMEMA/SP, Brazil.
Braz J Otorhinolaryngol. 2010 Nov-Dec;76(6):789-93. doi: 10.1590/S1808-86942010000600019.
Osteochondroplastic tracheobronchopathy (OT) is a rare benign disorder of the lower part of the trachea and the upper part of the main bronchus characterized by numerous submucosal calcified nodules, sessile, cartilaginous and/or osseous with laryngotracheobronchial lumen projection. There are less than 400 cases reported in the word literature.
to report and discuss 02 cases of OT with a bibliography review.
we report on 02 cases with bibliography revision from MEDLINE, LILACS and PUBMED data.
observational, descriptive, case reports.
the symptoms result from airway obstruction, causing dry cough, dyspnea and recurrent respiratory tract infections. The diagnostic hypothesis is established by endoscopy of the upper airway (laryngo-tracheo-bronchoscopy), and the trachea/chest computed tomography is the best image exam to define tracheal nodule alterations. The differential diagnoses are papillomatosis, amyloidosis and sarcoidosis chondrosarcoma hamartoma and calcified paratracheal lymph nodes. There is no specific treatment and the prognosis is good. Surgery is restricted to moderate or severe airway obstructions. Otorhinolaryngologists must include OT in the differential diagnosis of cases of upper airway and tracheobronchial tree suggestive symptoms.
骨软骨成形性气管支气管病(OT)是一种罕见的良性疾病,发生于气管下部和主支气管上部,其特征为大量黏膜下钙化结节,无蒂、软骨性和/或骨性,伴有喉气管支气管腔突出。世界文献中报道的病例少于 400 例。
报告并讨论 02 例 OT 病例,并进行文献复习。
我们报告了 02 例病例,并对 MEDLINE、LILACS 和 PUBMED 数据进行了文献复习。
观察性、描述性、病例报告。
气道阻塞导致症状,引起干咳、呼吸困难和反复呼吸道感染。上呼吸道内镜(喉气管支气管镜)可建立诊断假设,而气管/胸部计算机断层扫描是定义气管结节改变的最佳影像学检查。鉴别诊断包括乳头状瘤病、淀粉样变性和结节病、软骨肉瘤错构瘤和钙化性气管旁淋巴结。没有特定的治疗方法,预后良好。手术仅限于中度或重度气道阻塞。耳鼻喉科医生必须将 OT 纳入上呼吸道和气管支气管树疑似症状的鉴别诊断中。