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气管支气管骨软骨化生

Tracheobronchopathia osteochondroplastica.

作者信息

Silveira Mara Graziele Maciel, Castellano Maria Vera Cruz de Oliveira, Fuzi Clarice Emiko, Coletta Ester Nei Aparecida Martins, Spinosa Guilherme Nogueira

机构信息

. Serviço de Clínica Médica, Hospital do Servidor Público Estadual de São Paulo, São Paulo (SP) Brasil.

. Serviço de Doenças do Aparelho Respiratório, Hospital do Servidor Público Estadual de São Paulo, São Paulo (SP) Brasil.

出版信息

J Bras Pneumol. 2017 Mar-Apr;43(2):151-153. doi: 10.1590/S1806-37562016000000143.

DOI:10.1590/S1806-37562016000000143
PMID:28538784
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5474380/
Abstract

Tracheobronchopathia osteochondroplastica is a rare benign disease, of unknown cause, characterized by numerous sessile, cartilaginous, or bony submucosal nodules distributed throughout the anterolateral walls, projecting into the laryngotracheobronchial lumen. In general, tracheobronchopathia osteochondroplastica is diagnosed incidentally during bronchoscopy or autopsy and is not associated with a specific disease. We report the case of a male patient who was diagnosed with tracheobronchopathia osteochondroplastica via bronchoscopy and biopsy. RESUMO A traqueobroncopatia osteocondroplástica é uma doença benigna rara, de causa desconhecida, caracterizada por numerosos nódulos submucosos sésseis, cartilaginosos e/ou ósseos, distribuídos pelas paredes anterolaterais da traqueia, projetando-se no lúmen laringotraqueobrônquico. Em geral, a traqueobroncopatia osteocondroplástica é descoberta acidentalmente durante broncoscopias ou em necropsias e não é associada a uma doença específica. Relatamos o caso de um paciente que foi diagnosticado com traqueobroncopatia osteocondroplástica por broncoscopia e biópsia.

摘要

骨软骨瘤样气管支气管病是一种罕见的良性疾病,病因不明,其特征是在整个前外侧壁有许多无柄的、软骨性或骨性的黏膜下结节,突出到喉气管支气管腔内。一般来说,骨软骨瘤样气管支气管病是在支气管镜检查或尸检时偶然诊断出来的,与特定疾病无关。我们报告一例男性患者,通过支气管镜检查和活检被诊断为骨软骨瘤样气管支气管病。摘要:骨软骨瘤样气管支气管病是一种罕见的良性疾病,病因不明,其特征是在气管前外侧壁有许多无柄的、软骨性和/或骨性的黏膜下结节,突出到喉气管支气管腔内。一般来说,骨软骨瘤样气管支气管病是在支气管镜检查或尸检时偶然发现的,与特定疾病无关。我们报告一例通过支气管镜检查和活检被诊断为骨软骨瘤样气管支气管病的患者。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af17/5474380/a87e83e4344e/1806-3713-jbpneu-43-02-00151-gf3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af17/5474380/ebe28f149ca2/1806-3713-jbpneu-43-02-00151-gf1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af17/5474380/00d5db112de0/1806-3713-jbpneu-43-02-00151-gf2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af17/5474380/a87e83e4344e/1806-3713-jbpneu-43-02-00151-gf3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af17/5474380/ebe28f149ca2/1806-3713-jbpneu-43-02-00151-gf1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af17/5474380/00d5db112de0/1806-3713-jbpneu-43-02-00151-gf2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/af17/5474380/a87e83e4344e/1806-3713-jbpneu-43-02-00151-gf3.jpg

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Tracheobronchopathia osteochondroplastica. An underrecognized entity?骨软骨瘤病性气管支气管病。一种未被充分认识的疾病?
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Tracheobronchopathia osteochondroplastica: a rare large airway disorder.骨软骨瘤病性气管支气管病:一种罕见的大气道疾病。
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Laryngoscope Investig Otolaryngol. 2025 Feb 4;10(1):e70093. doi: 10.1002/lio2.70093. eCollection 2025 Feb.
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Tracheobronchopathia osteochondroplastica complicated with a pulmonary adenocarcinoma: A rare case report.骨软骨瘤病性气管支气管病合并肺腺癌:一例罕见病例报告
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