[骨软骨成形性气管支气管病：5例]

[Osteochondroplastic tracheobronchopathy: 5 cases].

作者信息

Saint-Blancard P, Natali F, Vaylet F, Coutant G, L'Her P, Le Vagueresse R

机构信息

Service d'anatomie pathologique, hôpital d'instruction des Armées Percy, Clamart, France.

出版信息

Rev Med Interne. 1997;18(11):882-7. doi: 10.1016/s0248-8663(97)81962-5.

DOI:10.1016/s0248-8663(97)81962-5

PMID:9499989

Abstract

Five new cases of tracheobronchopathia osteochondroplastica (TBOCP) are reported and clinical, radiological and pathological features are reviewed. TBOCP is a rare disease characterized by cartilaginous and bony nodules lining the mucosa of the trachea and major bronchi. The endoscopic features realize pathological evolution by stadiums. The prognosis is usually favourable. The etiology of TBOCP remains unknown, even though some cases were reported in association with amyloidosis.

摘要

本文报告了5例新的骨软骨瘤样气管支气管病（TBOCP）病例，并对其临床、放射学和病理学特征进行了回顾。TBOCP是一种罕见疾病，其特征为气管和主支气管黏膜内衬有软骨和骨结节。内镜特征可按阶段体现病理演变。预后通常良好。尽管有一些病例报告与淀粉样变性有关，但TBOCP的病因仍然不明。