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一例酷似严重主动脉瓣狭窄的特发性主动脉炎病例。

A case of idiopathic aortitis mimicking severe aortic stenosis.

作者信息

Lee Sang-Hee, Choi Jung-Hyun

机构信息

Division of Cardiology, Department of Internal Medicine, Yeungnam University College of Medicine, Daegu, Korea.

出版信息

J Cardiovasc Ultrasound. 2010 Dec;18(4):165-8. doi: 10.4250/jcu.2010.18.4.165. Epub 2010 Dec 31.

Abstract

Aortitis is the all-encompassing pathological term ascribed to inflammation of the aorta. Regardless of the etiology, it frequently results in aortic root dilatation and aortic insufficiency rather than aortic stenosis. The rare case of aortitis such as isolated idiopathic aortitis may occur without evidence of systenic inflammatory disease or infection, and usually has subclinical nature. Even though the goals of therapy include immediate treatment of aortic inflammation or infection, the optimal management of isolated idiopathic aortitis is uncertain. We report a rare case of isolated idiopathic aortitis mimicking acute severe aortic stenosis, which was improved after steroid therapy.

摘要

主动脉炎是用于描述主动脉炎症的一个综合性病理学术语。无论病因如何,它常导致主动脉根部扩张和主动脉瓣关闭不全,而非主动脉瓣狭窄。罕见的主动脉炎病例,如孤立性特发性主动脉炎,可能在无全身炎症性疾病或感染证据的情况下发生,且通常具有亚临床性质。尽管治疗目标包括立即治疗主动脉炎症或感染,但孤立性特发性主动脉炎的最佳管理尚不确定。我们报告一例罕见的孤立性特发性主动脉炎,其表现类似急性重度主动脉瓣狭窄,经类固醇治疗后病情改善。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3316/3021899/e08cd59b66e6/jcu-18-165-g001.jpg

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