Tizard Centre, University of Kent, Canterbury, Kent, UK.
J Autism Dev Disord. 2012 Feb;42(2):201-9. doi: 10.1007/s10803-011-1229-6.
Fragile X syndrome (FXS) and Smith-Magenis syndrome (SMS) are associated with a number of specific topographies of problem behavior. Very few studies have examined the function served by problem behavior in these groups. Using the Questions About Behavioral Function scale Matson and Vollmer (User's guide: questions about behavioral function (QABF). Scientific Publishers Inc., Baton Rouge, LA, 1995) the current study examined group differences in the function of problem behavior displayed by children with FXS and SMS, in comparison to a control group of children with non-specific intellectual and developmental disabilities. Between-group analyses showed children with SMS were more likely to display problem behavior related to physical discomfort. Both within- and between-group analyses showed children with FXS were less likely to display attention-maintained problem behavior. These findings hold implications for the assessment, treatment and prevention of problem behavior associated with both FXS and SMS.
脆性 X 综合征 (FXS) 和 Smith-Magenis 综合征 (SMS) 与许多特定类型的行为问题有关。很少有研究检查过这些群体中行为问题所起的作用。本研究使用行为功能问题问卷 (Matson 和 Vollmer, 1995) 比较了 FXS 和 SMS 儿童与非特定智力和发育障碍儿童的行为问题的功能的组间差异。组间分析表明，SMS 儿童更有可能表现出与身体不适相关的行为问题。无论是在组内还是组间分析中，都表明 FXS 儿童不太可能表现出注意力维持型的行为问题。这些发现对 FXS 和 SMS 相关行为问题的评估、治疗和预防具有重要意义。
