Division of Urology, Department of Surgery, Shin-Kong WHS Memorial Hospital, Taipei, Taiwan, ROC.
J Chin Med Assoc. 2011 Jul;74(7):325-8. doi: 10.1016/j.jcma.2011.05.010. Epub 2011 Jul 13.
Extramammary Paget's disease is an uncommon intra-epidermal malignant neoplasm that arises in area rich in apocrine glands. Common sites of occurrence include the vulva, perianal region, perineum, and scrotum. The lesion may be accompanied by an invasive adenocarcinoma or adenocarcinoma in situ of the apocrine glands. Generally, the prognosis is poor. Herein, we report two cases of extramammary Paget's disease, one involving the penoscrotal area with bilateral inguinal and pelvic lymph node metastases, the other involving the scrotal area without metastases.
派杰氏病是一种罕见的表皮内恶性肿瘤，发生于大汗腺丰富的区域。常见的发病部位包括外阴、肛周区域、会阴和阴囊。病变可伴有大汗腺的浸润性腺癌或原位腺癌。一般来说，预后较差。本文报告了 2 例派杰氏病，1 例累及阴茎阴囊区，伴双侧腹股沟和盆腔淋巴结转移，另 1 例累及阴囊区，无转移。
