Kiyochi Hidenori, Okada Kenzo, Iwakawa Kazuhide, Nakanishi Mamoru, Satoh Hajime, Iimori Shunsuke, Miyoshi Maiko, Yamamoto Koji, Kotegawa Hiroshi, Takai Akihiro, Kajiwara Shinsuke
Department of Surgery, Uwajima City Hospital, Uwajima, Japan.
Case Rep Gastroenterol. 2008 Sep;2(3):479-85. doi: 10.1159/000176062. Epub 2008 Dec 2.
Ciliated hepatic foregut cysts (CHFCs) are rare congenital cystic lesion that are most often solitary, unilocular, and located in the subcapsular region of the medial segment of the left hepatic lobe. The mucoid fluid contents affect imaging studies and often make definitive diagnosis difficult. CHFCs are usually asymptomatic and found incidentally. We report a 69-year-old female patient with a CHFC causing obstructive jaundice, which was difficult to differentiate from a biliary cystic neoplasm. A well-defined cystic lesion measuring 25 mm in diameter was located in the porta hepatis region. The lesion was densely adherent to the left and right hepatic ducts, riding on the bifurcation, and the common hepatic duct was extrinsically compressed. An extended left hepatectomy was performed. A diagnosis of CHFC was made on the basis of typical histological findings. CHFC should be included in the differential diagnosis for cystic lesions of the liver.
纤毛性肝前肠囊肿（CHFCs）是一种罕见的先天性囊性病变，通常为单发、单房，位于左肝叶内侧段的包膜下区域。其黏液样内容物影响影像学检查，常使明确诊断困难。CHFCs通常无症状，多为偶然发现。我们报告一例69岁女性患者，其CHFC导致梗阻性黄疸，难以与胆管囊性肿瘤相鉴别。一个边界清晰、直径25mm的囊性病变位于肝门区。该病变与左右肝管紧密粘连，骑跨于肝门分叉处，肝总管受到外在压迫。遂行扩大左肝切除术。根据典型的组织学表现确诊为CHFC。CHFC应纳入肝脏囊性病变的鉴别诊断。
