Vadiati Saberi B, Shakoorpour A
Postgraduate Student, Department of Periodontology, School of Dentistry, Babol University of Medical Sciences, Babol, Iran.
J Dent (Tehran). 2011 Spring;8(2):90-5. Epub 2011 Jun 30.
To report the oral findings, including dental anomalies, ectopic eruption of the maxillary permanent first molars and periodontal disease and soft tissue alterations, in a subject with Apert syndrome. Clinical and radiographic examination of a patient with Apert syndrome, aged 21 years old, not previously submitted for orthodontic or orthognathic treatment.Dental anomalies were present in a patient. Intraoral evaluation revealed poor oral hygiene with varying degrees of periodontal involvement, an arched swelling (pseudo cleft configuration), class III malocclusion, anterior open bite, posterior crossbite, supernumerary teeth, ectopic eruption and creamy white enamel opacities, an excessively large appearing tongue and a v-shaped maxillary arch. The occurrence of typical lateral palatal swellings agrees with the literature. The high prevalence of dental anomalies and ectopic eruption may suggest a possible etiologic relationship with the syndrome.
报告1名患有Apert综合征患者的口腔检查结果，包括牙齿异常、上颌第一恒磨牙异位萌出、牙周疾病及软组织改变。对1名21岁未曾接受过正畸或正颌治疗的Apert综合征患者进行临床及影像学检查。该患者存在牙齿异常。口内检查发现口腔卫生较差，伴有不同程度的牙周病变、拱形肿胀（假性腭裂形态）、III类错颌、前牙开颌、后牙反颌、多生牙、异位萌出及乳白色牙釉质混浊，舌体显得过大，上颌弓呈V形。典型的腭部侧方肿胀的出现与文献报道相符。牙齿异常及异位萌出的高发生率可能提示与该综合征存在某种病因学关联。
