Kim Jeong Ho, Kim Min-Ok, Choi Young Jin, Han Hyun Young, Park Kang Seo, Cho Byung Sun, Kang Dong Wook
Department of Medicine, Eulji University Hospital, Eulji University College of Medicine, Daejeon, Korea.
J Korean Surg Soc. 2011 Jun;80 Suppl 1(Suppl 1):S43-6. doi: 10.4174/jkss.2011.80.Suppl1.S43. Epub 2011 Jun 17.
Neurofibromatosis type 1 (NF-1) is a genetically inherited disorder that may cause skin abnormalities and tumors that form on nerve tissues. These tumors can be small or large and can occur anywhere in the body, including the brain, spinal cord, or other peripheral nerves. Retroperitoneal lymphangiomas are very rare benign malformations of the lymphatic system. About 95% lymphangiomas occur in the skin and the subcutaneous tissues of the head, neck and axillary region and the remaining 5% appear in other parts of the body such as lungs, pleura, pericardium, liver, gallbladder, kidney, and the mesentery. Herein, we report the case of a giant retroperitoneal lymphangioma in a patient with NF-1 with a review of the literature.
1型神经纤维瘤病（NF-1）是一种遗传性疾病，可能导致皮肤异常以及在神经组织上形成的肿瘤。这些肿瘤大小不一，可发生于身体的任何部位，包括脑、脊髓或其他周围神经。腹膜后淋巴管瘤是非常罕见的淋巴系统良性畸形。约95%的淋巴管瘤发生于头、颈、腋窝区域的皮肤和皮下组织，其余5%出现在身体的其他部位，如肺、胸膜、心包、肝、胆囊、肾和肠系膜。在此，我们报告1例患有NF-1的巨大腹膜后淋巴管瘤患者的病例，并对相关文献进行综述。
