Mona Ahmadi, Sevil Agabalaey Rafi, Zhale Faham, Ramin Azhough, Samad Beheshty Rooy, Omid Rahmani, Department of General Surgery and Pathology, Imam Reza Hospital, Azadi Street, Tabriz 5156975389, Iran.
World J Gastrointest Surg. 2011 Oct 27;3(10):156-8. doi: 10.4240/wjgs.v3.i10.156.
Degos' disease, otherwise known as "malignant atrophic papulosis" is a rare vasculopathy with an unknown etiology characterized by typical cutaneous lesions. Involvement of the gastrointestinal (GI) tract is observed in approximately half of patients and small infarctions in the mucosa can cause perforation and resulting peritonitis, the leading cause of death. We present a fatal case of Degos' disease with skin and GI involvement, manifesting as recurrent intestinal perforations and peritonitis, in a 15-year-old Iranian boy.
德戈斯病，又称“恶性萎缩性丘疹病”，是一种病因不明的罕见血管病，其特征为典型的皮肤损害。约半数患者胃肠道（GI）受累，小的黏膜梗死可导致穿孔和腹膜炎，这是导致死亡的主要原因。我们报告了一例德戈斯病致死病例，该病例为 15 岁伊朗男孩，皮肤和胃肠道受累，表现为反复发作的肠穿孔和腹膜炎。
