Serum carnitine level in phenylketonuric children under dietary control in Greece.
作者信息
Schulpis K H, Nounopoulos C, Scarpalezou A, Bouloukos A, Missiou-Tsagarakis S
机构信息
Institute of Child Health, Aghia Sophia Children's Hospital, Athens, Greece.
出版信息
Acta Paediatr Scand. 1990 Oct;79(10):930-4. doi: 10.1111/j.1651-2227.1990.tb11354.x.
Abstract
Although total, free and esterified carnitine blood levels were found to be low (p less than 0.001) in phenylketonuric patients under dietary treatment compared to controls, no clinical signs of carnitine deficiency were noticed. Exclusion from the PKU diet of nutrients rich in carnitine has been suggested. Supplementation of the diets with carnitine or preferably enrichment of the PKU formulas with carnitine will rectify the restriction of extrinsic carnitine in PKU dietary treatment.
摘要
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