Zhang Jason Chao, Bakir Belal, Lee Andrew, Yalamanchili Sushma S
Ophthalmology Department, The Methodist Hospital, Houston, Texas, United States.
BMJ Case Rep. 2011 Oct 16;2011:bcr0820114721. doi: 10.1136/bcr.08.2011.4721.
The Chiari I malformation is a congenital abnormality characterised by downward displacement of the cerebellar tonsils through the foramen magnum into the cervical spine. It presents clinically most often in young adult women. Known ocular manifestations linked to Chiari I consist primarily of oculomotor paresis with cranial nerve VI palsy and convergence/divergence abnormalities. Papilloedema is a rare manifestation of Chiari I with a clinical presentation often similar to that of idiopathic intracranial hypertension. To highlight this unusual complication, the authors report a 64-year-old female who developed papilloedema as the only presenting neurological symptom resulting from a Chiari I malformation.
Chiari I畸形是一种先天性异常，其特征是小脑扁桃体通过枕骨大孔向下移位至颈椎。它在临床上最常出现在年轻成年女性中。与Chiari I相关的已知眼部表现主要包括动眼神经麻痹伴第六脑神经麻痹以及集合/散开异常。视乳头水肿是Chiari I的一种罕见表现，其临床表现通常与特发性颅内高压相似。为了突出这种不寻常的并发症，作者报告了一名64岁女性，她因Chiari I畸形出现视乳头水肿作为唯一的神经系统症状。
