一名12岁女孩胆总管囊肿引发的癌症。

Cancer arising in a choledochal cyst in a 12-year-old girl.

作者信息

Iwai N, Deguchi E, Yanagihara J, Iwai M, Matsuo H, Todo S, Imashuku S

机构信息

Division of Surgery, Children's Research Hospital, Prefectural University of Medicine, Japan.

出版信息

J Pediatr Surg. 1990 Dec;25(12):1261-3. doi: 10.1016/0022-3468(90)90525-e.

DOI:10.1016/0022-3468(90)90525-e

PMID:2286901

Abstract

An adenocarcinoma was found in a choledochal cyst in a 12-year-old girl. This is the youngest patient so far reported with an adenocarcinoma in a choledochal cyst. The cyst consisted of dilatations of the intrahepatic bile ducts and the extrahepatic bile duct. Most of the cyst wall was resected. However, resection of the distal part of the cyst wall in the infrapancreatic region was impossible because of invasion of the portal vein and the inferior vena cava. This patient is now being treated with chemotherapy. We believe that early diagnosis is mandatory, and that total excision of a choledochal cyst is advisably to prevent the development of carcinoma.

摘要

在一名12岁女孩的胆总管囊肿中发现了腺癌。这是迄今为止报道的患有胆总管囊肿腺癌的最年轻患者。囊肿由肝内胆管和肝外胆管扩张组成。大部分囊肿壁被切除。然而，由于门静脉和下腔静脉受侵，无法切除胰下区域囊肿壁的远端部分。该患者目前正在接受化疗。我们认为早期诊断是必要的，并且建议对胆总管囊肿进行完全切除以预防癌症的发生。