Department of Cell Biology and Anatomy, University of Miami Miller School of Medicine, Miami, Florida, United States of America.
PLoS One. 2012;7(9):e44335. doi: 10.1371/journal.pone.0044335. Epub 2012 Sep 4.
Pharmacological agents, such as bezafibrate, that activate peroxisome proliferator-activated receptors (PPARs) and PPAR γ coactivator-1α (PGC-1α) pathways have been shown to improve mitochondrial function and energy metabolism. The mitochondrial DNA (mtDNA) mutator mouse is a mouse model of aging that harbors a proofreading-deficient mtDNA polymerase γ. These mice develop many features of premature aging including hair loss, anemia, osteoporosis, sarcopenia and decreased lifespan. They also have increased mtDNA mutations and marked mitochondrial dysfunction. We found that mutator mice treated with bezafibrate for 8-months had delayed hair loss and improved skin and spleen aging-like phenotypes. Although we observed an increase in markers of fatty acid oxidation in these tissues, we did not detect a generalized increase in mitochondrial markers. On the other hand, there were no improvements in muscle function or lifespan of the mutator mouse, which we attributed to the rodent-specific hepatomegaly associated with fibrate treatment. These results showed that despite its secondary effects in rodent's liver, bezafibrate was able to improve some of the aging phenotypes in the mutator mouse. Because the associated hepatomegaly is not observed in primates, long-term bezafibrate treatment in humans could have beneficial effects on tissues undergoing chronic bioenergetic-related degeneration.
药理制剂,如苯扎贝特,通过激活过氧化物酶体增殖物激活受体(PPARs)和过氧化物酶体增殖物激活受体 γ 共激活因子-1α(PGC-1α)途径,已被证明能改善线粒体功能和能量代谢。线粒体 DNA(mtDNA)突变体小鼠是一种具有缺乏校对功能的 mtDNA 聚合酶 γ 的衰老模型小鼠。这些小鼠表现出许多衰老特征,包括脱发、贫血、骨质疏松、肌肉减少症和寿命缩短。它们还具有增加的 mtDNA 突变和明显的线粒体功能障碍。我们发现,用苯扎贝特治疗 8 个月的突变体小鼠脱发延迟,并改善了皮肤和脾脏的衰老样表型。尽管我们观察到这些组织中脂肪酸氧化标志物增加,但我们没有检测到线粒体标志物的普遍增加。另一方面,突变体小鼠的肌肉功能或寿命没有改善,我们认为这归因于与纤维醇治疗相关的啮齿动物特有的肝肿大。这些结果表明,尽管苯扎贝特在啮齿动物肝脏中有次要作用,但它能够改善突变体小鼠的一些衰老表型。由于在灵长类动物中没有观察到相关的肝肿大,人类长期使用苯扎贝特治疗可能对经历慢性生物能相关退化的组织有有益的影响。