Chaabouni Ahmed, Rebai Nouri, Fourati Mohamed, Rekik Sami, Chabchoub Kamel, Slimen Mourad Hadj, Bahloul Ali, Mhiri Mohamed Nabil
Department of Urology, Habib Bourguiba, University Hospital Majida Boulila Road, Sfax 3029, Tunisia.
Int J Surg Case Rep. 2012;3(12):587-9. doi: 10.1016/j.ijscr.2012.01.013. Epub 2012 Mar 30.
Cystic lymphangioma is a rare benign vascular tumor that may arise in various sites, revealed at any age. Abdominal locations represent less than 10% of the cases preferentially involving the mesentery. We report a case of primary lymphangioma arising from the kidney.
A 50-year-old woman was admitted for severe left lumbar pain. Abdominal ultrasonography and computed tomography revealed a 6×10 cm multiloculated cystic mass with hydronephrosis, extending along the left renal hilum. Surgical exploration revealed a retroperitoneal cystic tumor. Anatomopathologic examination concluded it to be a cystic lymphangioma.
The cystic lymphangioma is a benign malformative tumor of the lymphatic system. Surgery is the best curative treatment with complete excision, the prognosis is excellent.
Primary renal lymphangioma is exceedingly rare. Medical imaging has certain limits for the diagnosis which required histological confirmation. The treatment of choice is surgical.
囊性淋巴管瘤是一种罕见的良性血管肿瘤，可发生于各个部位，可在任何年龄出现。腹部发病部位占病例不到10%，主要累及肠系膜。我们报告一例起源于肾脏的原发性淋巴管瘤。
一名50岁女性因严重左腰痛入院。腹部超声和计算机断层扫描显示一个6×10厘米的多房性囊性肿块伴肾积水，沿左肾门延伸。手术探查发现一个腹膜后囊性肿瘤。解剖病理学检查确诊为囊性淋巴管瘤。
囊性淋巴管瘤是一种淋巴管系统的良性畸形肿瘤。手术是最佳的治愈性治疗方法，完整切除后预后良好。
原发性肾淋巴管瘤极为罕见。医学影像诊断有一定局限性，需要组织学证实。首选治疗方法是手术。
