Manschot W A
Institute of Pathology, Erasmus University, Rotterdam, The Netherlands.
Br J Ophthalmol. 1990 Jan;74(1):56-8. doi: 10.1136/bjo.74.1.56.
The clinical and histopathological findings in a case of morning glory syndrome are described. Axial optic nerve retrodisplacement into a peripapillary scleral ectasia (staphyloma), absence of fibrous lamina cribrosa, and optic nerve atrophy were associated with various other, non-inherent ocular developmental anomalies. The uninterrupted lining of the inner wall of the staphyloma by one-layered, normal retinal pigment epithelium proves that the syndrome is not due to a neuroectodermal closure defect.
本文描述了一例牵牛花综合征的临床和组织病理学表现。轴性视神经向后移位至视乳头周围巩膜扩张(葡萄肿),筛板纤维层缺失,以及视神经萎缩与各种其他非先天性眼部发育异常相关。葡萄肿内壁由单层正常视网膜色素上皮连续覆盖,证明该综合征并非由神经外胚层闭合缺陷引起。