CHU Timone Marseille, France.
Arch Cardiovasc Dis. 2012 Nov;105(11):605-13. doi: 10.1016/j.acvd.2012.04.005. Epub 2012 Oct 4.
Adult patients with congenital heart disease (ACHD) represent a growing population due to progress in management. Surgical procedures generally fall short of restoring entirely normal anatomical and functional relations. Further procedures can be needed and lifelong follow-up is required. The right ventricle (RV) plays an important role in congenital heart disease and cardiac magnetic resonance (CMR) imaging has become the imaging method of choice for its assessment. CMR can provide relatively accurate measurements of RV volume and function, and arterial flow, with additional anatomical information provided by three-dimensional contrast angiography and late gadolinium imaging of fibrosis. Here we focus our review on three categories of ACHD in which evaluation of the RV is important: repaired tetralogy of Fallot, the systemic RV and Ebstein anomaly. We demonstrate how CMR contributes to decision-making regarding the types and timings of interventions. A dedicated CMR service should be regarded as a necessary facility of a centre specializing in the care of ACHD patients.
成人先天性心脏病(ACHD)患者由于治疗的进步而不断增加。手术通常无法完全恢复正常的解剖和功能关系。可能需要进一步的手术,并且需要终身随访。右心室(RV)在先天性心脏病中起着重要作用,心脏磁共振(CMR)成像已成为评估其的首选成像方法。CMR 可以提供 RV 容积和功能以及动脉血流的相对准确测量值,并通过三维对比血管造影和纤维化晚期钆成像提供额外的解剖信息。在这里,我们重点关注 RV 评估很重要的三种 ACHD 类型:修复性法洛四联症、系统性 RV 和埃布斯坦畸形。我们展示了 CMR 如何有助于决策干预的类型和时间。专门的 CMR 服务应被视为专门治疗 ACHD 患者的中心的必要设施。