Mancuso Andrea, Martinelli Luigi, De Carlis Luciano, Rampoldi Antonio Gaetano, Magenta Giovanni, Cannata Aldo, Belli Luca Saverio
Andrea Mancuso, Luca Saverio Belli, Epatologia e Gastroenterologia, Ospedale Niguarda Cà Granda, Piazza Ospedale Maggiore 3, 20162 Milano, Italy.
World J Hepatol. 2013 May 27;5(5):292-5. doi: 10.4254/wjh.v5.i5.292.
Transjugular intrahepatic portosystemic shunt (TIPS) is the standard treatment of Budd-Chiari syndrome (BCS) non responsive to medical therapy. However, patients with inferior vena cava (IVC) obstruction proximal to the atrium do not benefit from TIPS and a surgical approach is mandatory. We report the case of BCS due to intrapericardial IVC obstruction. We describe a novel surgical approach using a fresh caval homograft. An attempt to balloon dilatation of the IVC obstruction was complicated by right atrial disruption with tamponade and ventricular fibrillation. Lately, the patient successfully underwent a reconstruction of the cavo-atrial continuity by the interposition of a fresh caval homograft, a novel surgical approach never described before for BCS. Further follow-up revealed progressive reduction and resolution of ascites, and overall clinical improvement. IVC obstruction near to the atrium can be surgically approached with a new technique consisting in inferior vena cava resection and replacement with a caval homograft.
经颈静脉肝内门体分流术(TIPS)是药物治疗无效的布加综合征(BCS)的标准治疗方法。然而,心房近端下腔静脉(IVC)梗阻的患者无法从TIPS中获益,必须采用手术方法。我们报告了一例因心包内IVC梗阻导致的BCS病例。我们描述了一种使用新鲜腔静脉同种异体移植物的新型手术方法。对IVC梗阻进行球囊扩张的尝试因右心房破裂伴心包填塞和心室颤动而复杂化。最近,患者通过插入新鲜腔静脉同种异体移植物成功进行了腔房连续性重建,这是一种此前从未用于BCS的新型手术方法。进一步随访显示腹水逐渐减少并消退,整体临床状况改善。靠近心房的IVC梗阻可通过一种新技术进行手术治疗,该技术包括切除下腔静脉并用腔静脉同种异体移植物进行置换。