Beer William M, Carstairs Shaun D
Department of Emergency Medicine, Naval Medical Center, San Diego, California.
J Emerg Med. 2013 Oct;45(4):541-3. doi: 10.1016/j.jemermed.2013.03.035. Epub 2013 Jun 27.
Herlyn Werner Wunderlich Syndrome (HWWS) is a congenital abnormality of the Müllerian duct system resulting in uterovaginal duplication, obstructive hemivagina, and ipsilateral renal agenesis. It typically presents shortly after menarche with gradual onset of progressive pelvic pain.
We report a case of a 19-year-old female who presented to the Emergency Department with sudden onset of severe vaginal pain that was determined to be due to hematocolpos; imaging confirmed the diagnosis of HWWS.
To the best of our knowledge abrupt onset of vaginal pain due to HWWS has not been reported previously. We present this case to increase awareness among emergency physicians of this rare and interesting entity.
赫林-韦纳-温德利希综合征（HWWS）是苗勒管系统的一种先天性异常，导致子宫阴道重复畸形、梗阻性半阴道和同侧肾缺如。它通常在初潮后不久出现，渐进性盆腔疼痛逐渐发作。
我们报告一例19岁女性，因突发严重阴道疼痛就诊于急诊科，诊断为阴道积血；影像学检查确诊为HWWS。
据我们所知，此前尚未有HWWS导致突发阴道疼痛的报道。我们呈现此病例以提高急诊医生对这一罕见且有趣病症的认识。
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