Gungor Baris, Alper Ahmet T, Celebi Ahmet, Bolca Osman
Department of Cardiology, Siyami Ersek Thoracic and Cardiovascular Surgery Center, Training and Research Hospital, Istanbul, Turkey.
Indian Pacing Electrophysiol J. 2013 Aug 1;13(4):157-61. doi: 10.1016/s0972-6292(16)30651-9. eCollection 2013.
Left ventricular noncompaction (LVNC) is a genetically heterogenous form of cardiomyopathy which may remain undiagnosed till adulthood due to the late presentation of typical symptoms such as dyspnea, congestion, ventricular arrhythmias and thromboembolism. Symptomatic bradycardia secondary to persistent sinus node dysfunction is very rare. Coexistent cardiac defects are common in children however in adults the disease is usually in isolated form. Here, we present a case of twenty-three year-old female LVNC patient with patent ductus arteriosus, bicuspid aortic valve and persistent sinus node dysfunction who presented with dizziness as the first manifestation of the disease.
左心室心肌致密化不全（LVNC）是一种具有遗传异质性的心肌病，由于诸如呼吸困难、充血、室性心律失常和血栓栓塞等典型症状出现较晚，可能直到成年才被诊断出来。继发于持续性窦房结功能障碍的症状性心动过缓非常罕见。儿童中并存心脏缺陷很常见，但在成人中该疾病通常为孤立形式。在此，我们报告一例23岁女性LVNC患者，伴有动脉导管未闭、二叶式主动脉瓣和持续性窦房结功能障碍，其以头晕作为该疾病的首发表现。
