Kasperkiewicz Michael, Tukaj Stefan, Gembicki Anna-Julia, Silló Pálma, Görög Anna, Zillikens Detlef, Kárpáti Sarolta
Department of Dermatology, University of Lübeck, Ratzeburger Allee 160, 23538, Lübeck, Germany,
Cell Stress Chaperones. 2014 Nov;19(6):837-43. doi: 10.1007/s12192-014-0507-6. Epub 2014 Mar 19.
Heat shock proteins (Hsp) are highly conserved immunomodulatory molecules upregulated when cells are exposed to stressful stimuli, such as inflammation. Their involvement in various autoimmune diseases, including autoimmune bullous diseases and celiac disease, has been increasingly recognized. To further study the role of Hsp in autoimmune bullous diseases, we have investigated for the first time the humoral autoimmune response to Hsp40, Hsp60, Hsp70, and Hsp90 in patients with dermatitis herpetiformis (DH; n = 26), bullous pemphigoid (BP; n = 23), and pemphigus vulgaris (PV; n = 16), the first representing a cutaneous manifestation of celiac disease. While in patients with active BP and PV, serum levels of autoantibodies against these Hsp did not differ from the corresponding age- and gender-matched healthy controls (n = 9-14); circulating autoantibodies against Hsp60, Hsp70, and Hsp90 were found to be increased at the active disease stage of DH. Further analysis of this latter patient subgroup showed that these anti-Hsp autoantibodies decreased in parallel with serum autoantibodies against epidermal and tissue transglutaminase during remission of skin lesions following a gluten-free diet, revealing significantly positive correlations. Although further studies on larger groups of patients will be needed to confirm the present data, our results support the notion that autoantibodies against Hsp60, Hsp70, and Hsp90 deserve attention in the study of the mechanisms that promote the development and maintenance of DH and possibly also the underlying celiac disease as well as potential novel disease biomarkers.
热休克蛋白(Hsp)是高度保守的免疫调节分子,当细胞暴露于诸如炎症等应激刺激时会上调。它们参与包括自身免疫性大疱性疾病和乳糜泻在内的各种自身免疫性疾病,这一点已得到越来越多的认识。为了进一步研究Hsp在自身免疫性大疱性疾病中的作用,我们首次调查了疱疹样皮炎(DH;n = 26)、大疱性类天疱疮(BP;n = 23)和寻常型天疱疮(PV;n = 16)患者对Hsp40、Hsp60、Hsp70和Hsp90的体液自身免疫反应,其中DH是乳糜泻的一种皮肤表现形式。虽然在活动性BP和PV患者中,针对这些Hsp的自身抗体血清水平与年龄和性别匹配的健康对照(n = 9 - 14)没有差异;但发现在DH的活动期疾病阶段,针对Hsp60、Hsp70和Hsp90的循环自身抗体增加。对后一组患者亚群的进一步分析表明,在无麸质饮食后皮肤病变缓解期间,这些抗Hsp自身抗体与针对表皮和组织转谷氨酰胺酶的血清自身抗体平行下降,显示出显著的正相关。尽管需要对更大规模的患者群体进行进一步研究以证实目前的数据,但我们的结果支持这样一种观点,即针对Hsp60、Hsp70和Hsp90的自身抗体在促进DH以及可能还有潜在的乳糜泻的发生和维持的机制研究以及潜在的新型疾病生物标志物方面值得关注。