Oli Saurav Sen, Sapkota Shova, Bajagain Rupa, Saha Rachana, Paudel Suman
Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.
JNMA J Nepal Med Assoc. 2024 Feb 29;62(271):214-216. doi: 10.31729/jnma.8520.
Herlyn-Werner-Wunderlich Syndrome is a very rare congenital malformation of the urogenital tract involving both the Mullerian and Wolffian ducts characterized by the triad uterine diadelphys, obstructed vagina, and unilateral renal agenesis. If not diagnosed on time it may progress to adverse gynecological complications making timely diagnosis and treatment crucial. We hereby present a 14-year girl with right flank pain diagnosed as Herlyn-Werner-Wunderlich Syndrome by ultrasound scan which was managed surgically with drainage of hydrocolpos and marsupialization of vaginal septum. On two weeks follow up patient had symptomatic improvement with no any complications.
赫林-韦尔纳-温德利希综合征是一种非常罕见的泌尿生殖道先天性畸形，涉及苗勒管和中肾管，其特征为三联征：双子宫、阴道梗阻和单侧肾缺如。如果不能及时诊断，可能会进展为不良的妇科并发症，因此及时诊断和治疗至关重要。我们在此报告一名14岁右侧腰痛女孩，经超声扫描诊断为赫林-韦尔纳-温德利希综合征，通过手术治疗，进行了阴道积水引流和阴道隔造袋术。术后两周随访，患者症状改善，无任何并发症。
