Černá Monika, Třeška Vladislav, Krčma Michal, Daum Ondřej, Šlauf František
Clinic of Surgery, Plzeň Teaching Hospital and Charles University Medical Faculty, Alej Svobody 80, 304 60, Plzeň - Lochotín, Czech Republic.
1st Clinic of Internal Medicine, Plzeň Teaching Hospital and Charles University Medical Faculty, Alej Svobody 80, 304 60, Plzeň - Lochotín, Czech Republic.
J Med Case Rep. 2015 Feb 2;9:3. doi: 10.1186/1752-1947-9-3.
Vascular malformations of the thyroid gland represent a very rare, often accidentally diagnosed, disease that in the case of eufunctional goitre may be the cause of mechanical neck syndrome. The authors present here the complex differential-diagnosis and treatment approach and stress the importance of histopathology for determining the final diagnosis.
Using various imaging methods (ultrasound, multidetector computed tomography of the neck), the cause of breathing difficulties in a 64-year-old old man from the Czech Republic with normal thyroid gland function was found to be an arteriovenous malformation of the left lobe of his thyroid gland, 80 × 70 × 55 mm in size, reaching retrosternally between the major arteries branching from his aortic arch and displacing his trachea 10mm to the right. In preparation for surgery, he underwent a radio-interventional procedure with embolisation of the arteries supplying the left lobe. This was followed by a lobectomy on the left via a partial sternotomy. The definitive histology result confirmed that the arteriovenous malformation was the benign cause of the mechanical neck syndrome.
The case report presented here extends the differential diagnostic options in cases of mechanical neck syndrome. It describes a very rare disease of the thyroid gland, which prior to surgery may arouse suspicion of malignancy. It stresses the importance of close team cooperation between the endocrinologist, interventional radiologist and surgeon within the framework of preoperative diagnosis as well as preparation for surgery. Determination of the definitive histopathological diagnosis requires a pathologist experienced in such issues.
甲状腺血管畸形是一种非常罕见的疾病,常为偶然诊断,在甲状腺功能正常的甲状腺肿病例中,可能是机械性颈部综合征的病因。作者在此介绍复杂的鉴别诊断和治疗方法,并强调组织病理学对确定最终诊断的重要性。
通过多种影像学方法(超声、颈部多排螺旋计算机断层扫描),发现一名来自捷克共和国的64岁甲状腺功能正常男性呼吸困难的原因是其甲状腺左叶的动静脉畸形,大小为80×70×55毫米,在主动脉弓分支的主要动脉之间向后纵隔延伸,并将气管向右推移10毫米。在准备手术时,他接受了放射性介入治疗,对供应左叶的动脉进行栓塞。随后通过部分胸骨切开术进行了左侧甲状腺叶切除术。最终组织学结果证实动静脉畸形是机械性颈部综合征的良性病因。
本文呈现的病例报告扩展了机械性颈部综合征病例的鉴别诊断选项。它描述了一种非常罕见的甲状腺疾病,术前可能会引起对恶性肿瘤的怀疑。强调了内分泌科医生、介入放射科医生和外科医生在术前诊断及手术准备框架内密切团队合作的重要性。确定最终的组织病理学诊断需要一位在这类问题上经验丰富的病理学家。