Gupta Siddharth, Ahuja Puneet, Rehani Usha, Singh Vishal
Reader, Department of Oral Medicine, Diagnosis and Radiology, ITS Dental College, Hospital and Research Center, Greater Noida, Uttar Pradesh, India.
Principal, Professor and Head, Department of Oral Pathology and Microbiology, ITS Dental College, Hospital and Research Center, Greater Noida, Uttar Pradesh, India.
J Oral Biol Craniofac Res. 2011 Oct-Dec;1(1):47-9. doi: 10.1016/S2212-4268(11)60012-2.
Lymphangiomas are benign hamartomatous tumors of the lymphatic vessels. A lymphatic malformation is a congenital defect that occurs during early embryonic development when the lymphatic vessels do not properly form. The vessels may become blocked and enlarged as lymphatic fluid collects in the vessels, forming a mass or a cyst. About 50% of all lesions are noted at birth and around 90% develop by 2 years of age.
We report the case of lymphangioma, with an unusual presentation in the cheek region resulting into vestibular obliteration and expanding to the left maxilla diagnosed on the basis of histopathology. The review of literature concerning the clinical and histological features as well as the proper management concerning this hamartomatous entity is included.
The various treatment modalities for lymphangioma are surgical excision, radiation therapy cryotherapy, electrocautery, sclerotherapy, steroid administration, embolization, ligation, laser surgery with Nd-YAG and CO2 and radiofrequency tissue ablation technique. An early diagnosis and intervention helps in reducing the functional, psychological disturbances and cosmetic disfigurement.
淋巴管瘤是淋巴管的良性错构瘤性肿瘤。淋巴管畸形是一种先天性缺陷，发生于胚胎发育早期，此时淋巴管形成异常。随着淋巴液在血管中积聚，血管可能会堵塞并扩张，形成肿块或囊肿。所有病变中约50%在出生时被发现，约90%在2岁前出现。
我们报告了一例淋巴管瘤病例，其在颊部区域表现异常，导致前庭闭塞并扩展至左上颌骨，根据组织病理学确诊。文中还包括了关于该错构瘤实体的临床和组织学特征以及恰当治疗方法的文献综述。
淋巴管瘤的各种治疗方式包括手术切除、放射治疗、冷冻治疗、电灼、硬化治疗、类固醇给药、栓塞、结扎、Nd-YAG和CO2激光手术以及射频组织消融技术。早期诊断和干预有助于减少功能、心理障碍和外观毁损。
