Institute of Experimental Musculoskeletal Medicine (IEMM), University Hospital Muenster, Muenster, Germany.
Medical University of Vienna, Department of Internal Medicine III, Division of Rheumatology, Vienna, Austria.
Nat Med. 2015 Sep;21(9):1085-90. doi: 10.1038/nm.3917. Epub 2015 Aug 3.
Myostatin (also known as growth and differentiation factor 8) is a secreted member of the transforming growth factor-β (TGF-β) family that is mainly expressed in skeletal muscle, which is also its primary target tissue. Deletion of the myostatin gene (Mstn) in mice leads to muscle hypertrophy, and animal studies support the concept that myostatin is a negative regulator of muscle growth and regeneration. However, myostatin deficiency also increases bone formation, mainly through loading-associated effects on bone. Here we report a previously unknown direct role for myostatin in osteoclastogenesis and in the progressive loss of articular bone in rheumatoid arthritis (RA). We demonstrate that myostatin is highly expressed in the synovial tissues of RA subjects and of human tumor necrosis factor (TNF)-α transgenic (hTNFtg) mice, a model for human RA. Myostatin strongly accelerates receptor activator of nuclear factor κB ligand (RANKL)-mediated osteoclast formation in vitro through transcription factor SMAD2-dependent regulation of nuclear factor of activated T-cells (NFATC1). Myostatin deficiency or antibody-mediated inhibition leads to an amelioration of arthritis severity in hTNFtg mice, chiefly reflected by less bone destruction. Consistent with these effects in hTNFtg mice, the lack of myostatin leads to increased grip strength and less bone erosion in the K/BxN serum-induced arthritis model in mice. The results strongly suggest that myostatin is a potent therapeutic target for interfering with osteoclast formation and joint destruction in RA.
肌肉生长抑制素(也称为生长分化因子 8)是转化生长因子-β(TGF-β)家族的一种分泌成员,主要在骨骼肌中表达,骨骼肌也是其主要靶组织。在小鼠中删除肌肉生长抑制素基因(Mstn)会导致肌肉肥大,动物研究支持肌肉生长抑制素是肌肉生长和再生的负调节剂的概念。然而,肌肉生长抑制素缺乏也会增加骨形成,主要是通过对骨骼的负荷相关作用。在这里,我们报告了肌肉生长抑制素在破骨细胞形成和类风湿关节炎(RA)关节骨进行性丧失中的一个以前未知的直接作用。我们证明,肌肉生长抑制素在 RA 患者和人类肿瘤坏死因子(TNF)-α转基因(hTNFtg)小鼠的滑膜组织中高度表达,hTNFtg 小鼠是人类 RA 的模型。肌肉生长抑制素通过核因子激活的 T 细胞(NFATC1)的转录因子 SMAD2 依赖性调节,强烈加速核因子受体激活剂κB 配体(RANKL)介导的体外破骨细胞形成。肌肉生长抑制素缺乏或抗体介导的抑制导致 hTNFtg 小鼠关节炎严重程度的改善,主要表现为骨破坏减少。与 hTNFtg 小鼠的这些作用一致,缺乏肌肉生长抑制素可导致 K/BxN 血清诱导的关节炎模型中小鼠握力增加和骨侵蚀减少。这些结果强烈表明,肌肉生长抑制素是一种有效的治疗靶点,可干扰 RA 中的破骨细胞形成和关节破坏。