Solomon Missale, Bozic Molly, Mascarenhas Maria R
Drexel University Philadelphia, Philadelphia, PA, USA.
Pediatric Gastroenterology, Hepatology & Nutrition, Riley Hospital for Children, Indianapolis, IN, USA.
Clin Chest Med. 2016 Mar;37(1):97-107. doi: 10.1016/j.ccm.2015.11.009. Epub 2015 Dec 24.
The importance of maintaining adequate nutrition in patients with cystic fibrosis has been well known for the past 3 decades. Achieving normal growth and maintaining optimal nutrition is associated with improved lung function. Comprehensive and consistent nutritional assessments at regular intervals can identify those at risk of nutritional failure and uncover micronutrient deficiencies contributing to malnutrition. Management of malnutrition in cystic fibrosis should follow a stepwise approach to determine the causes and comorbidities and to develop a nutritional plan. Nutritional management is crucial at every stage in a person's life with cystic fibrosis and remains a cornerstone of management.
在过去三十年中，维持囊性纤维化患者充足营养的重要性已广为人知。实现正常生长并维持最佳营养状况与肺功能改善相关。定期进行全面且连贯的营养评估能够识别有营养衰竭风险的患者，并发现导致营养不良的微量营养素缺乏情况。囊性纤维化患者营养不良的管理应采取循序渐进的方法，以确定病因和合并症，并制定营养计划。在囊性纤维化患者生命的每个阶段，营养管理都至关重要，并且仍然是管理的基石。
