一名年轻女性的原发性乳腺血管肉瘤。
Primary breast angiosarcoma in a young woman.
作者信息
Iacoponi Sara, Calleja Jackie, Hernandez Gines, Sainz de la Cuesta Ricardo
机构信息
Gynecologic Oncology Unit. Quiron university hospital Madrid, Spain.
Gynecologic Oncology Unit. Quiron university hospital Madrid, Spain.
出版信息
Int J Surg Case Rep. 2016;24:101-3. doi: 10.1016/j.ijscr.2016.05.015. Epub 2016 May 18.
INTRODUCTION
Angiosarcomas of the breast are a rare subtype of sarcomas that frequently are diagnosed after radiation therapy for primary breast cancer. Primary angiosarcomas are rare entities accounting 0.05% of all malignant breast neoplasm.
PRESENTATION OF CASE
We report a case of primary angiosarcoma of the breast in a 25 years woman, with no previous radiotherapy, treated with a total mastectomy followed by radio-chemotherapy.
DISCUSSION
Total mastectomy appears to be the only treatment known that has proven to benefit these patients. Adjuvant treatment has not proven value up until today. The 5-year disease free survival for grade 1 tumors can be as high as 76%, and up to 15% for grade 3.
CONCLUSION
Due to the rarity of these tumors there is no standard therapies approach.
引言
乳腺血管肉瘤是肉瘤的一种罕见亚型，常在原发性乳腺癌放疗后被诊断出来。原发性血管肉瘤极为罕见，占所有乳腺恶性肿瘤的0.05%。
病例介绍
我们报告一例25岁女性原发性乳腺血管肉瘤病例，该患者既往未接受过放疗，接受了全乳切除术，随后进行放化疗。
讨论
全乳切除术似乎是目前已知唯一经证实对这些患者有益的治疗方法。迄今为止，辅助治疗尚未被证明有价值。1级肿瘤的5年无病生存率可达76%，3级肿瘤则高达15%。
结论
由于这些肿瘤罕见，尚无标准治疗方法。
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