Patibandla Mohana Rao, Thotakura Amit K, Uppin Megha, Challa Sundaram, Addagada Gokul Chowdary, Nukavarapu Manisha
Department of Neurosurgery, Nizam's Institute of Medical Sciences, Hyderabad, India.
NRI Medical College, Mangalagiri, Andra Pradesh, India.
Asian J Neurosurg. 2016 Jul-Sep;11(3):323. doi: 10.4103/1793-5482.145158.
Pilomyxoid astrocytoma (PMA) is a new entity described in WHO 2007 classification of brain tumors. Pilocytic astrocytoma (PA) and PMA share many histopathological features with a few differences in histopathology and behavior of the tumor. This tumor is commonly located in the hypothalamic chiasmatic region. PMA behaves more aggressively than PA, with shorter progression-free survival as well as a higher rate of recurrence and CNS dissemination. We describe a case of PMA in a 10-year-old male involving left parietal lobe presenting with raised ICP features along with the follow-up. Patient was symptom free after 7 months of postoperative and 5½ months of post-radiation. The unusual site and atypical Magnetic resonance imaging features are distinctive in this case report.
毛黏液样星形细胞瘤（PMA）是2007年世界卫生组织脑肿瘤分类中描述的一种新实体。毛细胞型星形细胞瘤（PA）和PMA具有许多组织病理学特征，在肿瘤的组织病理学和行为方面有一些差异。这种肿瘤通常位于下丘脑视交叉区域。PMA的行为比PA更具侵袭性，无进展生存期更短，复发率和中枢神经系统播散率更高。我们描述了一例10岁男性的PMA病例，累及左顶叶，表现为颅内压升高特征及随访情况。术后7个月和放疗后5个半月患者无症状。该病例报告中不寻常的部位和非典型的磁共振成像特征很独特。
