Byrd S E, Osborn R E, Bohan T P, Naidich T P
Department of Radiology, Children's Memorial Hospital, Northwestern University Medical School, Chicago, Illinois.
Pediatr Radiol. 1989;19(4):219-22. doi: 10.1007/BF02386836.
The migrational disorders are a rare group of congenital malformations of the brain. They consist of the following entities - lissencephaly (agyria - pachygyria), pachygyria, schizencephaly, heterotopia and polymicrogyria. We studied 40 children with migrational disorders radiologically with CT and MR. This article (Part II) deals with our patients with schizencephaly, heterotopia and polymicrogyria. These patients presented clinically with a variety of symptoms. The most common were seizures, delayed development, failure to thrive and hydrocephalus. CT and MR both demonstrated the characteristic findings in all of our patients except the polymicrogyria group. The gray matter and cleft abnormalities seen in these disorders were demonstrated with CT and MR. However, MR provided better delineation of these disorders than CT. Because some forms of migrational disorders can be inherited, it is extremely important for the radiologist to understand the characteristic findings for correct diagnosis which is essential for parental counseling.
脑移行障碍是一组罕见的先天性脑畸形。它们包括以下疾病——无脑回畸形（光滑脑-巨脑回）、巨脑回、脑裂畸形、异位症和多小脑回畸形。我们对40例患有脑移行障碍的儿童进行了CT和MR影像学研究。本文（第二部分）涉及我们有关脑裂畸形、异位症和多小脑回畸形的患者。这些患者临床上表现出多种症状。最常见的是癫痫发作、发育迟缓、生长发育不良和脑积水。除多小脑回畸形组外，CT和MR均在我们所有患者中显示出特征性表现。这些疾病中所见的灰质和脑裂异常通过CT和MR得以显示。然而，MR对这些疾病的显示比CT更好。由于某些形式的脑移行障碍可能是遗传性的，放射科医生了解特征性表现以进行正确诊断极其重要，这对于向家长提供咨询至关重要。
