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迟发性脊椎骨骺发育不良的阿育吠陀疗法,一种罕见的遗传性疾病。

Ayurvedic management of spondyloepiphyseal dysplasia tarda, a rare hereditary disorder.

作者信息

Singh Sarvesh Kumar, Rajoria Kshipra

机构信息

P.G. Department of Panchakarma, National Institute of Ayurveda, Jaipur, 302002, Rajasthan, India.

S.S.S.B. Ayurvedic College and Hospital, Jaipur, 303603, Rajasthan, India.

出版信息

J Ayurveda Integr Med. 2016 Oct-Dec;7(4):249-254. doi: 10.1016/j.jaim.2016.10.002. Epub 2016 Nov 25.

DOI:10.1016/j.jaim.2016.10.002
PMID:27890699
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5192282/
Abstract

Spondyloepiphyseal dysplasia tarda (SEDT) is a rare genetic disease in which patient suffers from short stature, short trunk and neck with disproportionately long arms, coxa vara, skeletal features such as barrel shaped chest, kyphosis, scoliosis and early arthropathy. Only limited medical and surgical management is available in modern medicine. A 15 years old male suffering from SEDT and diagnosed as Vata vyadhi was treated with Panchakarma therapy and selected Ayurvedic oral medicines. Ayurvedic treatment was directed to ameliorate the orthopaedic clinical conditions in this case. Panchakarma procedures such as Shalishastika pinda svedana for a month and Mustadi yapana basti for 16 days were given along with oral Ayurvedic medicines. Same Panchakarma procedures were repeated after an interval of 2 months. A combination of Ayurvedic oral medicines such as Trayodashanga guggulu-500 mg twice a day, Dashmool kvatha (decoction of roots of 10 herbs) 40 ml twice a day, Eranda paka 10 g twice a day, Shiva gutika-500 mg twice a day and Dashmoolarista-20 ml (with equal water) twice a day were prescribed. Eight scales based Medical outcome study (MOS) - 36 item short form - health surveys was assessed for outcome which shows good improvement. Kyphosis, scoliosis and pain were moderately reduced. Clinical experience of this case indicates that Ayurvedic herbs along with Panchakarma can play a major role in the management of hereditary disorder SEDT.

摘要

迟发性脊椎骨骺发育不良(SEDT)是一种罕见的遗传性疾病,患者身材矮小、躯干和颈部短小,手臂相对较长,存在髋内翻,还有桶状胸、脊柱后凸、脊柱侧凸和早期关节病等骨骼特征。现代医学中针对该病的医疗和手术治疗手段有限。一名15岁患有SEDT且被诊断为瓦塔病(Vata vyadhi)的男性患者接受了潘查卡玛疗法(Panchakarma therapy)和精选的阿育吠陀口服药物治疗。在该病例中,阿育吠陀治疗旨在改善骨科临床状况。给予了诸如持续一个月的沙利沙斯蒂卡泥疗(Shalishastika pinda svedana)和持续16天的穆斯塔迪灌肠(Mustadi yapana basti)等潘查卡玛程序,同时服用阿育吠陀口服药物。两个月后重复相同的潘查卡玛程序。开具了以下阿育吠陀口服药物组合:十三味古古卢(Trayodashanga guggulu)——每日两次,每次500毫克;十味根汤(Dashmool kvatha,10种草药根的煎剂)——每日两次,每次40毫升;蓖麻膏(Eranda paka)——每日两次,每次10克;湿婆丸(Shiva gutika)——每日两次,每次500毫克;十味根酒(Dashmoolarista)——每日两次,每次20毫升(与等量水混合)。采用基于八项量表的医学结局研究(MOS)-36项简表-健康调查对结果进行评估,结果显示有明显改善。脊柱后凸、脊柱侧凸和疼痛程度均有适度减轻。该病例的临床经验表明,阿育吠陀草药与潘查卡玛疗法在遗传性疾病SEDT的治疗中可发挥重要作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/cb15784eacc0/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/2cf176b037c3/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/fdd4c14dec5b/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/10a347a4854c/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/9df4ef38931c/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/cb15784eacc0/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/2cf176b037c3/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/fdd4c14dec5b/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/10a347a4854c/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/9df4ef38931c/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/13a6/5192282/cb15784eacc0/gr5.jpg

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