幼年女性外阴侵袭性血管黏液瘤酷似阴蒂肥大

Aggressive Angiomyxoma of the Vulva Mimicking Clitoromegaly in a Young Child.

作者信息

Kawamura Masataka, Matsumoto Fumi, Matsui Futoshi, Yazawa Koji, Shimada Kenji

机构信息

Department of Urology, Osaka Medical Center and Research Institute for Maternal and Child Health, Osaka, Japan.

出版信息

Urology. 2017 Mar;101:142-144. doi: 10.1016/j.urology.2016.10.034. Epub 2016 Oct 28.

DOI:10.1016/j.urology.2016.10.034

PMID:27984053

Abstract

Aggressive angiomyxoma (AAM) is a rare soft tissue tumor of mesenchymal origin that chiefly involves the vulvar and perineal region. In 90% of cases, AAM presents in women of reproductive age with a peak incidence in the fourth decade of life. To date, AAM of the vulva in young children and infancy has never been reported. We present a case of AAM of the vulva that was initially interpreted as clitoromegaly in a 3-year-old girl.

摘要

侵袭性血管黏液瘤（AAM）是一种罕见的间叶组织起源的软组织肿瘤，主要累及外阴和会阴区域。90%的病例中，AAM发生于育龄女性，发病高峰在40岁左右。迄今为止，幼儿及婴儿期外阴AAM从未有过报道。我们报告一例3岁女童外阴AAM病例，最初被误诊为阴蒂肥大。